What is Cystic Fibrosis? – Definition, Symptoms, and Treatment

Oxygen Therapy

Cystic fibrosis (CF) affects about 30,000 Americans. Worldwide, about 70,000 to 100,000 people have this condition. It affects males and females at about the same rate. About 75 percent of new diagnoses happen before age 2. 1

What is Cystic Fibrosis?

What is Cystic Fibrosis?

CF is a genetic disorder that affects the respiratory and digestive systems. It affects the body’s cells, and causes the production of abnormally thick mucus, leading to the blockage of the pancreatic ducts, intestines, and bronchi and often resulting in respiratory infection.

What Are Cystic Fibrosis Symptoms?

Symptoms vary and can include:

  • Cough, shortness of breath and wheezing
  • chronic lung infections, including pneumonia and bronchitis
  • Inability to gain weight
  • frequent greasy, bulky stools or difficulty with bowel movements

What Are the Causes of Cystic Fibrosis?

Cystic fibrosis is a genetic disorder, so patients can only be born with the disease. About one in 25 of us carries the faulty gene that causes it, usually without knowing. The highest genetic risk factor for a child born with CF is when both parents carry the defective gene, which makes the disease rare.

What Happens After a Cystic Fibrosis Diagnosis?

While there is no cure for the disease, patients with this disease can manage their care effectively to live longer. To stay healthy, people of all ages with CF must follow a regular treatment routine. In addition to a nutrition and fitness plan, there are medications that reduce the mucus buildup that causes lung infections and regular use of antibiotics to fight infections once they start.

What are the Risk Factors and Complications Related to Cystic Fibrosis?

Since this condition is a genetic disease, family history is the main risk factor. However, there are also complications that come with having this disease that should not be ignored. Here are some examples of CF complications.

Respiratory Complications

  • Damaged Airways. Also known as bronchiectasis, this is a chronic lung condition that widens and scars the bronchial tubes, or airways. Widened and scarred bronchial tubes make it difficult to move breathing air in and out of a person’s lungs. CF is the leading cause of damaged airways.
  • Nasal Polyps. Nasal polyps can often grow in people who have CF. They are a cancerless growth on the lining of the nose or sinuses. However, this condition is common and can be treated with medication or surgery.
  • Respiratory Failure. Since CF affects the respiratory system, overtime a person may experience respiratory failure and damaged lung tissue. This can be considered life-threatening, and is the most common cause of death.

Digestive Complications

  • Diabetes. The thick mucus caused by cystic fibrosis can lead to pancreas scarring. Because of the scarring, the pancreas can not produce the normal amount of insulin a person needs, therefore causing diabetes. However, diabetes can be well managed with healthy eating, an active lifestyle, and medication.
  • Nutrition Deficiency. Also due to thick mucus, tubes that deliver digestive enzymes to your intestines may be blocked. Without digestive enzymes, your body can not absorb nutrition correctly, causing for weight loss and delayed growth.

Oxygen Therapy Treatment for Cystic Fibrosis

A key part of the regular treatment of this disease is oxygen therapy. Because of compromised lung function, patients with cystic fibrosis often suffer from fatigue. Weakened lungs produce lower levels of oxygen, which can also cause harm to the heart. Through the use of oxygen concentrators, oxygen therapy helps maintain healthy oxygen levels when the lungs cannot.

Conclusion

Patients with cystic fibrosis can rely on oxygen concentrators to help maintain consistent oxygen therapy. Find both home oxygen concentrators and portable oxygen concentrators at The Oxygen Concentrator Supplies Shop. Our knowledgeable staff can help select an oxygen concentrator that fits your therapy needs.

References

  1. Healthline. Cystic Fibrosis by the Numbers: Facts, Statistics, and You